Berry Syndrome, a Complex Aortopulmonary Malformation
Prenatal diagnosis by fetal echocardiography
a spotlight by s. gerboni
Berry syndrome is a rare association of distal aortopulmonary window (APW), aortic origin of the right pulmonary artery (RPA), intact ventricular septum, patent ductus arteriosus, and interrupted or hypoplastic aortic arch. Since the original description in 1982 as a specific syndrome rather than a random coincidence.
Criss-cross heart or â€˜upstairsâ€“downstairsâ€™ heart.
Review by S.Gerboni
Lev and Rowlatt in 1961 described unusual arrangement of the cardiac inlets :
ventricular chambers arranged in a superoinferior fashion,
with the RV superiorly and the LV inferiorly located.
The term Criss-cross heart,was introduced by Anderson et al. in
1974, defined as crossing of the long axes of the AV valves.
New Guidelines from the AHA on prevention of Infective Endocarditis
Extensively analysis of literature on procedure-related bacteriemia and infective endocarditis, results of profilactic studies in animals, and retrospective and prospective studies of the prevention of infective endocarditis.
Course in Cardiogenesis and Congenital Cardiopathies :
From Developmental Models to Clinical Applications
June 7th-10th 2008
The AEPC interventional working group is pleased to announce the second
TEACHING COURSE in pediatric and congenital INTERVENTIONAL CARDIAC
CATHETERISATION, which will take place on 4-5 april 2008, in Milan (Italy).
Aorto-ventricular tunnel is a congenital, extracardiac channel which connects the ascending aorta above the sinutubular junction to the cavity of the left, or (less commonly) right ventricle………………….>
Pentalogy of Cantrell is a rare congenital malformation
characterized by midline defects, resulting from
defective development in the septum transversum. The
constellation of findings includes deficiency of the
diaphragmatic pericardium, lower sternum, anterior
diaphragm, supraumbilical abdominal wall often
allowing an omphalocele as well as an intrapericardial
diaphragmatic hernia, and a cardiac lesion, most often
a ventricular septal defect. In severe cases, the
heart herniates through the diaphragmatic defect,
causing thoracoabdominal ectopia cordis. Other
associated congenital cardiac lesions may include an
atrial septal defect, pulmonary valve stenosis, tetralogy
of Fallot, dextrocardia, anomalous pulmonary venous
connection, tricuspid atresia, and truncus arteriosus.
Noncompaction of the ventricular myocardium (NCVM) is a rare cardiomyopathy characterized by
numerous, prominent trabeculations and deep intertrabecular recesses caused by arrest in myocardial embryogenesis.
This study reviews our experience with neonatal and fetal NCVM. In contrast to the past reports of fetal and
neonatal NCVM, all pts in this group improved, and survived infancy.