All posts in English


Warsaw, POLAND 3 – 5 NOVEMBER 2011

Dear Friends,
It is a great pleasure for me to advertise the first Course organized by the Fetal Cardiology Working Group and Cardiovascular Morphology Working Group of the Association of European Pediatric Cardiology in collaboration with the Agatowa Ultrasound Clinic.
A comprehensive course designed for the AEPC junior members, and all others who would like to to develop basic fetal echocardiography skills and find out the differences between pediatric and fetal examination. We are very busy fetal cardiology clinic so majority of defects will be demonstrated during “live-scanning” sessions.
We have the proposal to all participants to present their own interesting fetal cases.

I hope to see you in Warsaw.
Joanna Dangel, Course Director

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46th Annual Meeting of the Association for European Paediatric and Congenital Cardiology

Dear Friends and Colleagues,

Dear Friends and Colleagues, It is our pleasure to invite you to the 46th Annual Meeting of the Association for European Paediatric and Congenital Cardiology which will be held in Istanbul. We are pleased to organise this wonderful event for the second time in Istanbul after the 1976 meeting of AEPC. We believe this meeting will give you the opportunity to increase the knowledge exchange in paediatric and congenital cardiology. The meeting will cover all the aspects of this unique medical science.

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Fetal and Pediatric Cardiology Seminar in Paris

Fetal and Pediatric Cardiology Seminar in Paris
December 9th and 10th of 2011 – Paris – FRANCE

Dear Friends,

We propose this Seminar on fetal and pediatric cardiology. We meant it to be different. Indeed, the presentations will be delivered by Junior / Senior pairs. We hope you will find appealing and exciting this array of subjects ranging from genetics, embryology, first quarter imaging, 3D and 4D imaging and magnetocardiography to pathophysiology of the coronary flow and neurodevelopment, pathologies of the left side of the heart and surgical procedures.
We will usher you into a recent though highly innovative disciplines, with both the experience of the greatest international experts and the enthusiasm of junior practitioners, tomorrow’s seniors, to escort us. We will be speaking English: it is the language of scientific discourse, used in both debate and publications,but with available translation into French.



you can also copy it on google and save it in your favourites

hope to see you in Paris

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Atrioventricular Conduction in Fetuses Exposed to Maternal Anti-Ro/SSA and Anti-La/SSB Antibodies

Prolongation of the Atrioventricular Conduction in Fetuses Exposed to Maternal Anti-Ro/SSA and Anti-La/SSB Antibodies Did Not Predict Progressive Heart Block A Prospective Observational Study on the Effects of Maternal Antibodies on 165 Fetuses.

Jaeggi ET, Silverman ED, Laskin C, Kingdom J, Golding F, Weber R.

Division of Cardiology, Department of Pediatrics, The Hospital for Sick Children, University of Toronto, Toronto, Ontario, Canada; The Hospital for Sick Children Research Institute, University of Toronto, Toronto, Ontario, Canada.

J Am Coll Cardiol. 2011 Mar 29;57(13):1487-92.


OBJECTIVES: We prospectively examined the prevalence and outcome of untreated fetal atrioventricular (AV) prolongation in the presence of maternal anti-Ro antibodies.

BACKGROUND: It has been suggested that antibody-mediated congenital complete atrioventricular block (CAVB) may be preventable if detected and treated early when low-grade block is present. With this rationale in mind, dexamethasone has been advocated by others to treat prolonged fetal AV conduction >2 z-scores, consistent with first-degree heart block.

METHODS: Between July 2003 and June 2009, 165 fetuses of 142 anti-Ro/La antibody-positive women were referred to our center for serial echocardiography. Our protocol included weekly evaluation of the fetal AV conduction between 19 (range 17 to 23) and 24 (range 23 to 35) gestational weeks. AV times were compared with institutional reference data and with post-natal electrocardiograms.

RESULTS: Of 150 fetuses with persistently normal AV conduction throughout the observation period, a diagnosis of CAVB was subsequently made in 1 at 28 weeks, after the serial evaluation had ended. Of 15 untreated fetuses either with AV prolongation between 2 and 6 z-scores or with type 1 second-degree block, progressive heart block developed in none of them. Three of these 15 fetuses (20%) had a neonatal diagnosis of first-degree block that spontaneously resolved (n = 2) or has not progressed (n = 1) on follow-up examinations. No other cardiac complications were detected.

CONCLUSIONS: Fetal AV prolongation did not predict progressive heart block to birth. Our findings question the rationale of a management strategy that relies on the early identification and treatment of fetal AV prolongation to prevent CAVB.
Copyright © 2011 American College of Cardiology Foundation. Published by Elsevier Inc. All rights reserved.

J Am Coll Cardiol. 2011 Mar 29;57(13):1487-92.

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THE 20th International Parma Echo Meeting From Fetus to Young Adult

It is with great pleasure that we would like to announce:
THE 20th International Parma Echo Meeting
From Fetus to Young Adult

To be held at the at the University of Parma,
Parma Italy on June 22,23, 24, 2011

If you are interested in participating please contact the organizing

Secretariat at:
Via Gramsci, 14-43100 Parma, Italy
Tel: 39 0521 702201 – FAX 39 0521 702394

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4D Fetal Echocardiography (Ebook Open Access)

4D Fetal Echocardiography (Ebook Open Access)

Authors: Domenico Arduini, Giuseppe Rizzo

Preface Abstract:

The examination of the fetal heart is part of the comprehensive fetal scan, but this examination is still considered a challenge even for experienced sonographers. Over the years the number of ultrasound techniques used in fetal cardiology impressively increased and no other fetal organ is examined with as many modalities as the fetal heart including high resolution two dimensional (2D) imaging, M-mode examination, spectral, color, power, highdefinition digital Doppler, B flow as well as tissue Doppler. It is, however, common knowledge that despite the availability of all these technologies, screening programs, especially when limited to the study of the “four chamber view”, have shown disappointing low detection rates for congenital heart disease (CHD). Although the identification of CHD can be improved by routinely visualizing the outflow tracts, their diagnosis is greatly affected by the skill of the operator as well as his ability to interpret the findings.

Very recently three- and four- dimensional (3D and 4D) technologies have been introduced in fetal cardiology and have revolutionized the way in which it is possible to study the heart. 4D ultrasonography may reduce the operator dependency of CHD diagnosis and adds the possibility to obtain offline virtual planes in cardiac examinations, views of the fetal heart difficult or impossible to obtain with conventional 2D ultrasound.

This new fetal cardiology ebook, we believe, will be of great value for all practicing clinicians wanting to start the study of the fetal heart with 4D ultrasonography. We have chosen a panel of contributors that are both leaders in this field and can represent the differences in practice between Europe and United States This is a comprehensive guide intended for anyone interested in fetal heart scanning performing both routine screening ultrasonographic examinations and targeted heart scans. It aims to assist the reader with the following questions: how can I use this technology to acquire cardiac volumes?, how do I handle cardiac volume data sets after acquisition? , how can I improve diagnosis and definition of CHD?

It is our hope that this book will provide a bridge between scientists using and testing new technologies for research purposes and clinicians wishing to improve their daily practice.

Affiliation: Department of Obstetrics and Gynecology Universita Roma Tor Vergata Rome Italy

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5th European Echocardiography Course on Congenital Heart Disease

5th European Echocardiography Course on Congenital Heart Disease
6 – 9 October 2010

UCL Institute of Child Health, London

The Imaging Working Group of the Association of European Paediatric Cardiology (AEPC) in collaboration with the Working Group of Grown-up Congenital Heart Disease of the European Society of Cardiology (ESC) and the European Association of Echocardiography will organise the 5th European Echocardiography Course in Congenital Heart Disease this time in London, from Wednesday 6th to Saturday 9th October 2010.
The course will provide both theoretical and practical review of echocardiographic techniques used in the current era, including Tissue Doppler Imaging, speckle tracking in both 2D and 3D echocardiography and real time 3D echocardiography.

For the first time, there will be three parallel hands-on sessions on:

  • Transthoracic live scanning with patients
  • Transoesophageal scanning with simulators
  • 3D datasets postprocessing
  • As in the previous courses, a forum of distinguished speakers and appreciated teachers from all over Europe and overseas will share their experience with the audience.

    The number of participants is limited to 150, therefore we advise applicants to book early to guarantee a place on the course.

    For full programme, registration form and general information please go to

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Kabuki Syndrome

Kabuki Syndrome
a post_it by s.gerboni

Kabuki syndrome, also known as Kabuki makeup syndrome and Niikawa-Kuroki syndrome, was initially described in 1988 by Niikawa et al. Congenital heart disease is commonly associated with Kabuki syndrome, with a reported incidence of 31–58% in large series

Most patients with Kabuki syndrome have five cardinal features:

  1. distinct facial features,
  2. postnatal growth retardation,
  3. developmental delay or mental retardation,
  4. skeletal abnormalities,
  5. and dermatoglyphic abnormalities.

The diagnosis is determined clinically because the chromosomes are normal
and no clinical test exists to confirm the clinical diagnosis of Kabuki syndrome.
The association of cardiac defects with Kabuki syndrome has been well described. The majority of these
defects are isolated shunt lesions, conotruncal abnormalities, or various forms of arch obstruction.
The spectrum of associated cardiac defects is varied.
The finding of left-sided obstructive lesions, specifically coarctation of the aorta, is reported in up to 29% of cases and in my serie three patients have a Shone Sindrome. Only two cases of associated congenital heart disease with single-ventricle physiology have been reported.
Recently were reported a case series of three patients with Kabuki syndrome and single-ventricle physiology, specifically hypoplastic left heart syndrome (HLHS), from a single institution This complete and illustrates the full spectrum of left-sided obstructive lesions and expands the phenotype of cardiac defects associated with Kabuki syndrome.

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